Idiopathic calcification of basal ganglia and cerebellar dentate nucleus is synonymous with Fahr's disease, which is often an autosomal dominant, rarely occurring neurodegenerative disorder. Few sporadic autosomal recessive cases have also been described. Symptomatology of the Fahr's disease ranges from movement disorders, Parkinsonism like symptoms to cognitive defects. Majority of the cases reported were in adults with typical presentation. Here we report a rare occurrence of Fahr's disease in a young boy presented only with seizures.
